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22q11.2 deletion syndrome

ORPHA:567· ICD-10 D82.1

Definition

A rare chromosomal anomaly which causes a congenital malformation disorder that is typically characterized by cardiac defects, palatal anomalies, facial dysmorphism, developmental delay and immune deficiency.

Prevalence
1-5 / 10 000
Inheritance
Autosomal dominant
Age of onset
All ages