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Neurofibromatosis type 1

ORPHA:636· ICD-10 Q85.0

Definition

Neurofibromatosis type 1 (NF1) is a clinically heterogeneous, neurocutaneous genetic disorder characterized by café-au-lait spots, iris Lisch nodules, axillary and inguinal freckling, and multiple neurofibromas.

Prevalence
1-5 / 10 000
Inheritance
Autosomal dominant
Age of onset
Infancy, Neonatal