vitalwiki

葡萄糖-6-磷酸酶缺乏所致肝糖原贮积症

ORPHA:364· ICD-10 E74.0· Glycogen storage disease due to glucose-6-phosphatase deficiency

患病率
1-9 / 100 000
遗传方式
Autosomal recessive
发病年龄
Infancy, Neonatal