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磷酸烯醇式丙酮酸羧激酶缺乏症

ORPHA:2880· ICD-10 E74.4· Phosphoenolpyruvate carboxykinase deficiency

患病率
<1 / 1 000 000
遗传方式
Autosomal recessive, Mitochondrial inheritance
发病年龄
Infancy, Neonatal