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X-linked centronuclear myopathy

ORPHA:596· ICD-10 G71.2

Definition

A rare X-linked congenital myopathy characterized by numerous centrally placed nuclei on muscle biopsy and that presents at birth with marked weakness, hypotonia and respiratory failure.

Prevalence
Unknown
Inheritance
X-linked recessive
Age of onset
Antenatal, Neonatal