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Paternal 20q13.2q13.3 microdeletion syndrome

ORPHA:261304· ICD-10 Q93.5

Definition

Paternal 20q13.2q13.3 microdeletion syndrome is a recently described syndrome characterized by severe pre- and post-natal growth retardation, microcephaly, intractable feeding difficulties, mild psychomotor retardation, hypotonia and facial dysmorphism.

Prevalence
<1 / 1 000 000
Inheritance
Not applicable
Age of onset
Antenatal, Neonatal