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葡糖-6-磷酸酶缺乏所致糖原贮积症1a型

ORPHA:79258· ICD-10 E74.0· Glycogen storage disease due to glucose-6-phosphatase deficiency type Ia

患病率
Unknown
遗传方式
Autosomal recessive
发病年龄
Infancy, Neonatal