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原发性免疫缺陷伴自然杀伤细胞缺乏和肾上腺功能减退

ORPHA:75391· ICD-10 D84.8· Primary immunodeficiency with natural-killer cell deficiency and adrenal insufficiency

患病率
<1 / 1 000 000
遗传方式
Autosomal recessive
发病年龄
Childhood