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x连锁多内分泌腺病肠病伴免疫失调综合征

ORPHA:37042· ICD-10 E31.0· Immune dysregulation-polyendocrinopathy-enteropathy-X-linked syndrome

患病率
<1 / 1 000 000
遗传方式
X-linked recessive
发病年龄
Infancy, Neonatal