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白细胞介素7受体α缺乏所致T-B+重症联合免疫缺陷

ORPHA:169154· ICD-10 D81.2· T-B+ severe combined immunodeficiency due to IL-7Ralpha deficiency

患病率
1-9 / 1 000 000
遗传方式
Autosomal recessive
发病年龄
Infancy