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Хвороба Норрі

ORPHA:649· ICD-10 H35.5· Norrie disease

Визначення(English summary)

A rare developmental defect during embryogenesis characterized by abnormal retinal development with congenital blindness. Common associated manifestations include sensorineural hearing loss and developmental delay, intellectual disability and/or behavioral disorders.

Поширеність
<1 / 1 000 000
Успадкування
X-linked recessive
Вік початку
Antenatal, Neonatal