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ORPHA:319182· ICD-10 Q87.1· Wiedemann-Steiner syndrome

Визначення(English summary)

A rare, genetic multiple congenital anomalies/dysmorphic syndrome characterized by short stature, hypertrichosis (most commonly of the back or elbow regions), facial dysmorphism, behavioral problems, developmental delay and, most commonly, mild to moderate intellectual disability.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal dominant
Вік початку
Childhood, Infancy, Neonatal