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X-linked mendelian susceptibility to mycobacterial diseases

ORPHA:319605· ICD-10 D84.8

Definition

X-linked (XR) Mendelian susceptibility to mycobacterial diseases (MSMD) describes a rare group of immunodeficiencies due to specific mutations in the inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase gamma (IKBKG) or the cytochrome b-245, beta polypeptide (CYBB) genes. They are characterized by mycobacterial infections, occuring in males.

Prevalence
<1 / 1 000 000
Inheritance
X-linked recessive
Age of onset
Adolescent, Childhood, Infancy