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Tyrosinemia type 2

ORPHA:28378· ICD-10 E70.2

Definition

A rare inborn error of tyrosine metabolism characterized by hypertyrosinemia with oculocutaneous manifestations and, in some cases, intellectual deficit.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Adolescent, Childhood, Infancy, Neonatal