vitalwiki

Pancreatic insufficiency-anemia-hyperostosis syndrome

ORPHA:199337· ICD-10 E88.8

Definition

A rare syndromic mitochondrial disease characterized by exocrine pancreatic insufficiency, dyserythropoietic anemia, and calvarial hyperostosis.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal