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Acrofrontofacionasal dysostosis

ORPHA:1784· ICD-10 Q75.1

Definition

A rare congenital malformation syndrome characterized by the association of facial and skeletal anomalies with severe intellectual deficit and occasional genitourinary anomalies.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Neonatal