Нейроендокринна пухлина підшлункової залози
ORPHA:97253· Neuroendocrine tumor of pancreas
Визначення(English summary)
Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma) (see these terms).
- Поширеність
- 1-9 / 1 000 000
- Успадкування
- Autosomal dominant, Not applicable
- Вік початку
- Adult