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Синдром Трічера-Коллінза

ORPHA:861· ICD-10 Q75.4· Treacher-Collins syndrome

Визначення(English summary)

A rare genetic mandibulofacial dysostosis characterized by bilateral symmetrical oto-mandibular dysplasia including underdeveloped cheekbones (malar hypoplasia), a very small low jaw (micrognathia) and downward-slanting palpebral fissures, coloboma of the lower eyelids, microtia, hearing loss and without abnormalities of the extremities. Intelligence is normal.

Поширеність
1-9 / 1 000 000
Успадкування
Autosomal dominant, Autosomal recessive
Вік початку
Antenatal, Neonatal