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Синдром розщепленої кисті-розщепленої стопи-глухоти

ORPHA:71271· ICD-10 Q87.2· Split hand-split foot-deafness syndrome

Визначення(English summary)

Split hand - split foot - deafness is an extremely rare genetic syndrome reported in a few families to date and characterized clinically by split hand/split foot malformation (SHFM; see this term) and mild to moderate sensorineural hearing loss, sometimes associated with cleft palate and intellectual deficit.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal recessive
Вік початку
Infancy, Neonatal