Множинні ендокринні неоплазії, тип 1
ORPHA:652· ICD-10 D44.8· Multiple endocrine neoplasia type 1
Визначення(English summary)
A rare inherited cancer syndrome, characterized by the development of multiple neuroendocrine tumors of the parathyroids, gastro-entero-pancreatic tract, and anterior pituitary gland, and less commonly the adrenal cortical gland, thymus and bronchi, with other non-endocrine tumors in some patients.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Autosomal dominant, Not applicable
- Вік початку
- All ages