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GNE міопатія

ORPHA:602· ICD-10 G71.8· GNE myopathy

Визначення(English summary)

GNE myopathy is a rare autosomal recessive distal myopathy characterized by early adult-onset, slowly to moderately progressive distal muscle weakness that preferentially affects the tibialis anterior muscle and that usually spares the quadriceps femoris. Muscle biopsy reveals presence of rimmed vacuoles.

Поширеність
1-9 / 100 000
Успадкування
Autosomal dominant, Autosomal recessive
Вік початку
Adolescent, Adult