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Ідіопатичний стероїдорезистентний нефротичний синдром

ORPHA:567548· ICD-10 N04.8· Idiopathic steroid-resistant nephrotic syndrome

Визначення(English summary)

A rare, idiopathic nephrotic syndrome characterized by the triad of proteinuria, hypoalbuminemia and edema in patients who do not respond, or only partially respond, to the initial trial of corticosteroids. Patients may be multidrug resistant or may be sensitive to second-line immunosuppressive therapy.

Поширеність
1-9 / 1 000 000
Вік початку
Adolescent, Adult, Childhood