Легенева венооклюзивна хвороба та/або легеневий капілярний гемангіоматоз

Визначення(English summary)

A disorder that constitutes a rare subgroup of rare pulmonary hypertension characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction.