vitalwiki

Внутрішньопротокова папілярна муцинозна карцинома підшлункової залози

ORPHA:424058· ICD-10 C25.3· Intraductal papillary mucinous carcinoma of pancreas

Визначення(English summary)

Intraductal papillary mucinous carcinoma of pancreas is a rare epithelial tumor of pancreas characterized by malignant, mucin-producing cystic mass, originating from the pancreatic ductal system, associated with local invasion and metastatic spread, composed of mucin-producing, columnar epithelial cells covering the dilated pancreatic ducts with a papillary structure. The presenting symptoms are non-specific and include abdominal pain, pancreatitis, steatorrhea, jaundice and diabetes. Many patients are asymptomatic at the time of diagnosis.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult