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Первинна дистонія, тип DYT17

ORPHA:370103· ICD-10 G24.1· Primary dystonia, DYT17 type

Визначення(English summary)

Primary dystonia, DYT17 type is a rare, genetic, isolated dystonia initially presenting as torticollis, and later progressing to segmental or generalized dystonia. Dysphonia and dysarthria also occur later in the disease course.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal recessive
Вік початку
Adolescent, Adult