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Дизембріопластична нейроепітеліальна пухлина

ORPHA:251946· ICD-10 D33.0· Dysembryoplastic neuroepithelial tumor

Визначення(English summary)

A rare mixed neuronal-glial tumor characterized by a benign, usually supratentorial lesion with predominantly cortical location and multinodular architecture. The tumor typically becomes symptomatic in the second or third decade of life with drug-resistant partial seizures. Histological hallmark is the specific glioneuronal element, columns oriented perpendicularly to the cortical surface, formed by bundles of axons attached to oligodendroglia-like cells, while neurons appear to float in an abundant eosinophilic matrix.

Успадкування
Not applicable
Вік початку
All ages