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Non-distal deletion 12q syndrome

ORPHA:96160· ICD-10 Q93.5

Definition

A partial autosomal monosomy characterized by variable combination of developmental delay, intellectual disability, ectodermal, genitourinary and minor cardiac anomalies, and specific dysmorphic features (prominent forehead and low-set ears). Specific combination depends on the size and breakpoints of deleted regions.

Age of onset
Neonatal