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Apert syndrome

ORPHA:87· ICD-10 Q87.0

Definition

A frequent form of acrocephalosyndactyly, a group of inherited congenital malformation disorders, characterized by craniosynostosis, midface hypoplasia, and finger and toe anomalies and/or syndactyly.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
Antenatal, Neonatal