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Congenital lactic acidosis, Saguenay-Lac-Saint-Jean type

ORPHA:70472· ICD-10 G31.8

Definition

A rare degenerative mitochondrial disease characterized by chronic metabolic acidosis, hypotonia, facial dysmorphism and delayed development.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal