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SYNGAP1-related developmental and epileptic encephalopathy

ORPHA:544254· ICD-10 G40.4

Definition

A rare genetic developmental and epileptic encephalopathy (DEE) characterized by developmental delay, generalized epilepsy consisting of eyelid myoclonia with absences and myoclonic-atonic seizures, intellectual disability and autism spectrum disorder (ASD).

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Infancy