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Gorlin syndrome

ORPHA:377· ICD-10 C44.9

Definition

A rare hereditary disorder due to autosomal dominant transmission with hamartosis characterized by multiple early-onset basal cell carcinoma (BCC), multiple jaw keratocysts and skeletal abnormalities.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
Adolescent, Adult