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T-B+ severe combined immunodeficiency due to JAK3 deficiency

ORPHA:35078· ICD-10 D81.2

Definition

Severe combined immunodeficiency (SCID) T-B+ due to JAK3 deficiency is a form of SCID characterized by severe and recurrent infections, associated with diarrhea and failure to thrive.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal