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Osteopenia-intellectual disability-sparse hair syndrome

ORPHA:2324· ICD-10 Q87.5

Definition

A rare syndrome characterized by sparse hair, osteopenia, intellectual disability, minor facial abnormalities, joint laxity and hypotonia. There have been no further descriptions in the literature since 1992.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal