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Joubert syndrome with renal defect

ORPHA:220497· ICD-10 Q04.3

Definition

Joubert syndrome with renal defect is a rare subtype of Joubert syndrome and related disorders (JSRD) characterized by the neurological features of JS associated with renal disease, in the absence of retinopathy.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal