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Syndactyly-telecanthus-anogenital and renal malformations syndrome

ORPHA:140952· ICD-10 Q87.8

Definition

A rare malformation syndrome characterized by the association of toe syndactyly, facial dysmorphism including telecanthus (abnormal distance between the eyes) and a broad nasal tip, urogenital malformations and anal atresia.

Prevalence
<1 / 1 000 000
Inheritance
X-linked dominant
Age of onset
Infancy, Neonatal