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3β-羟基类固醇脱氢酶缺乏所致先天性肾上腺皮质增生症

ORPHA:90791· ICD-10 E25.0· Congenital adrenal hyperplasia due to 3-beta-hydroxysteroid dehydrogenase deficiency

患病率
<1 / 1 000 000
遗传方式
Autosomal recessive
发病年龄
Infancy, Neonatal