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牙本质发育不全-身材矮小-听力丧失-智力障碍综合征

ORPHA:71267· ICD-10 Q87.8· Dentinogenesis imperfecta-short stature-hearing loss-intellectual disability syndrome

患病率
<1 / 1 000 000
遗传方式
Autosomal recessive
发病年龄
Infancy, Neonatal