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鱼鳞病-肝脾肿大-小脑退化综合征

ORPHA:2274· ICD-10 Q87.8· Ichthyosis-hepatosplenomegaly-cerebellar degeneration syndrome

患病率
<1 / 1 000 000
遗传方式
Autosomal recessive, X-linked recessive
发病年龄
Infancy, Neonatal