АКТГ-залежний синдром Кушинга
ORPHA:99892· ICD-10 E24.0· ACTH-dependent Cushing syndrome
Визначення(English summary)
A group of endogenous Cushing syndrome (CS) caused by abnormal production of ACTH due, in 80% of cases, to adrenocorticotropic hormone (ACTH) oversecretion by a pituitary adenoma (Cushing disease, CD) and in 20% of cases to ectopic ACTH secretion (CS due to EAS) by an extrapituitary tumor or very rarely due to a tumor secreting both ACTH and corticotrophin-releasing hormone (CRH).
- Поширеність
- 1-9 / 1 000 000