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Хвороба Дента, тип 1

ORPHA:93622· ICD-10 N25.8· Dent disease type 1

Визначення(English summary)

A rare X-linked monogenic renal tubular disease, characterized by manifestations of complex proximal tubule dysfunction with low-molecular-weight (LMW) proteinuria, hypercalciuria, nephrolithiasis, nephrocalcinosis, and progressive renal failure. Extra-renal involvement is absent.

Поширеність
Unknown
Успадкування
X-linked recessive
Вік початку
Childhood