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Синдромна діарея

ORPHA:84064· ICD-10 K52.8· Trichohepatoenteric syndrome

Визначення(English summary)

A rare gastroenterologic disease manifesting as intractable diarrhea in the first month of life with failure to thrive and associated with facial dysmorphism, hair abnormalities, and, in some cases, immune disorders and intrauterine growth restriction.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal recessive
Вік початку
Antenatal, Infancy, Neonatal