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Злоякісний атрофічний папулез

ORPHA:679· ICD-10 I77.8· Malignant atrophic papulosis

Визначення(English summary)

Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal dominant
Вік початку
Adult