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Мономелічна аміотрофія

ORPHA:65684· ICD-10 G12.8· Monomelic amyotrophy

Визначення(English summary)

Monomelic amyotrophy (MA) is a rare benign lower motor neuron disorder characterized by muscular weakness and wasting in the distal upper extremities during adolescence followed by a spontaneous halt in progression and a stabilization of symptoms.

Поширеність
Unknown
Успадкування
Unknown
Вік початку
Adolescent, Adult