Мономелічна аміотрофія
ORPHA:65684· ICD-10 G12.8· Monomelic amyotrophy
Визначення(English summary)
Monomelic amyotrophy (MA) is a rare benign lower motor neuron disorder characterized by muscular weakness and wasting in the distal upper extremities during adolescence followed by a spontaneous halt in progression and a stabilization of symptoms.
- Поширеність
- Unknown
- Успадкування
- Unknown
- Вік початку
- Adolescent, Adult