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Синдром Вайля-Маркесані

ORPHA:3449· ICD-10 Q87.0· Weill-Marchesani syndrome

Визначення(English summary)

Weill-Marchesani syndrome (WMS) is a rare condition characterized by short stature, brachydactyly, joint stiffness, and characteristic eye abnormalities including microspherophakia, ectopia of the lens, severe myopia, and glaucoma.

Поширеність
1-9 / 100 000
Успадкування
Autosomal dominant, Autosomal recessive
Вік початку
Infancy, Neonatal