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Weill-Marchesani syndrome

ORPHA:3449· ICD-10 Q87.0

Definition

A rare connective tissue disorder characterized by acromelic short stature, joint stiffness, stiff and thick skin, and characteristic eye abnormalities including microspherophakia, ectopia lentis, severe myopia, and glaucoma.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant, Autosomal recessive
Age of onset
Infancy, Neonatal