Синдром TEMPI
ORPHA:284227· ICD-10 D47.2· TEMPI syndrome
Визначення(English summary)
TEMPI syndrome is a rare multi-systemic disease characterized by the presence of Telangiectasias, Erythrocytosis with elevated erythropoietin levels, Monoclonal gammopathy, Perinephric-fluid collections, and Intrapulmonary shunting.
- Поширеність
- <1 / 1 000 000
- Вік початку
- Adult