Вроджена вада розвитку легеневих дихальних шляхів, тип 3
ORPHA:280847· ICD-10 Q33.0· Congenital pulmonary airway malformation type 3
Визначення(English summary)
A rare subtype of congenital pulmonary airway malformation characterized by a multicystic mass of non-functioning lung tissue consisting of numerous microcysts of less than 0.5 cm in diameter. The lesions have intracystic communications, can be connected to the tracheobronchial tree, and are usually unilateral, involving an entire lobe. The condition may be associated with polyhydramnios, fetal hydrops, and stillbirth, or present with severe respiratory distress in the neonatal period.
- Вік початку
- Antenatal, Neonatal