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Мікроформа голопрозенцефалії

ORPHA:280200· ICD-10 Q04.2· Microform holoprosencephaly

Визначення(English summary)

A benign form of holoprosencephaly characterized by midline defects without the typical HPE defect in brain cleavage and which can variably manifest with microcephaly, hypotelorism, midline cleft lip and/or flat nose, choanal stenosis, pyriform sinus stenosis, coloboma as well as a single median maxillary incisor.

Поширеність
1-9 / 100 000
Успадкування
Multigenic/multifactorial
Вік початку
Childhood, Infancy, Neonatal