Спадкова аритмогенна кардіоміопатія
ORPHA:247· Inherited arrhythmogenic cardiomyopathy
Визначення(English summary)
A heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias and a risk of sudden cardiac death.
- Поширеність
- 1-5 / 10 000
- Успадкування
- Autosomal dominant, Autosomal recessive
- Вік початку
- Adolescent, Adult