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Синдром KBG

ORPHA:2332· ICD-10 Q87.8· KBG syndrome

Визначення(English summary)

A rare congenital malformation syndrome characterized by a typical facial dysmorphism, macrodontia of the permanent upper central incisors, short stature, skeletal anomalies, developmental delay and behavioral abnormalities.

Поширеність
<1 / 1 000 000
Успадкування
Autosomal dominant
Вік початку
Adolescent, Childhood, Infancy, Neonatal